血液疾患と輸血ジャーナル

概要

Portal Vein Thrombosis and Budd-Chairi Syndrome Due to In-apparent Polycythaemia Vera: Case Report

Shah Kajal*, Panchal Harsha, Patel Apurva

Portal vein thrombosis (PVT) is an uncommon finding in patients without cirrhosis. The underlying aetiology is challenging and Budd-Chiari syndrome is caused by occlusion of the hepatic veins that drain the liver. It presents with the classical triad of abdominal pain, ascites, and liver enlargement. The main cause of this syndrome is represented by myeloproliferative diseases and, in particular, by polycythaemia vera. The latter may cause multiple splanchnic thrombosis, including portal vein thrombosis, particularly important for its clinical outcomes of ascites, oesophageal varices, collateral vessels genesis, etc. We describe a case of 37 year male presented with severe abdominal pain, abdominal distension due to portal vein thrombosis and budd chairi syndrome caused by polycythaemia vera.